EULAR/PRINTO/PRES - mandatory histology or angiographic abnormality PLUS ≥1 of five features.
The Childhood Polyarteritis Nodosa Criteria is a rheumatology scoring tool used in paediatric practice. EULAR/PRINTO/PRES - mandatory histology or angiographic abnormality PLUS ≥1 of five features. It scores 6 criteria and interprets the total across 3 bands, so the number always arrives with the severity it implies rather than on its own. In PediAid each criterion is shown as a labelled option with the weight it carries, so the total can be checked rather than taken on trust.
6. They are MANDATORY - Necrotising vasculitis on biopsy OR angiographic abnormality (aneurysm/stenosis/occlusion); Skin involvement - livedo reticularis, nodules, superficial or deep infarcts; Myalgia or muscle tenderness; Hypertension for age; Peripheral neuropathy - sensory or motor mononeuritis multiplex; Renal involvement - proteinuria, haematuria or impaired renal function.
The total is interpreted as: any score - Criteria not met: the mandatory histological or angiographic criterion is absent - childhood PAN cannot be classified; 4 criteria or more - Mandatory only: histology/angiography present but no additional feature yet - at least one of the five clinical criteria is required; 5 criteria or more - Criteria MET: classifies as childhood polyarteritis nodosa (sensitivity 89.6%, specificity 99.6%). Treat with corticosteroids plus cyclophosphamide in severe disease; assess for hepatitis B.
No. It is a structured way to record and communicate severity. A clinician concerned about a child should act on that concern regardless of the total.
Source: Ozen S et al. EULAR/PRINTO/PRES Ankara 2008 criteria. Ann Rheum Dis 2010;69:798-806.
Yes. Score definitions are bundled with the PediAid app, so the score computes without a connection.