ACR criteria - ≥4 of 6 features classify EGPA.
The Eosinophilic Granulomatosis with Polyangiitis (Churg-Strauss) is a rheumatology scoring tool used in paediatric practice. ACR criteria - ≥4 of 6 features classify EGPA. It scores 6 criteria and interprets the total across 2 bands, so the number always arrives with the severity it implies rather than on its own. In PediAid each criterion is shown as a labelled option with the weight it carries, so the total can be checked rather than taken on trust.
6. They are Asthma; Eosinophilia > 10 % on differential white cell count; Mononeuropathy or polyneuropathy; Migratory or transient pulmonary infiltrates on imaging; Paranasal sinus abnormality; Biopsy containing a blood vessel with extravascular eosinophils.
The total is interpreted as: any score - Criteria not met: fewer than 4 criteria - does not classify as EGPA; 4 criteria or more - Criteria MET: ≥4 of 6 criteria - classifies as EGPA (sensitivity 85%, specificity 99.7%). Assess for cardiac involvement, which drives mortality.
No. It is a structured way to record and communicate severity. A clinician concerned about a child should act on that concern regardless of the total.
Rare in children; asthma and eosinophilia usually precede the vasculitic phase.
Yes. Score definitions are bundled with the PediAid app, so the score computes without a connection.