PRES/ACR/EULAR paediatric criteria - the mandatory major criterion plus ≥2 of 20 minor criteria.
The Juvenile Systemic Sclerosis Criteria is a rheumatology scoring tool used in paediatric practice. PRES/ACR/EULAR paediatric criteria - the mandatory major criterion plus ≥2 of 20 minor criteria. It scores 11 criteria and interprets the total across 3 bands, so the number always arrives with the severity it implies rather than on its own. In PediAid each criterion is shown as a labelled option with the weight it carries, so the total can be checked rather than taken on trust.
11. They are MAJOR (mandatory) - Proximal skin sclerosis/induration of the skin proximal to MCP or MTP joints; Cutaneous - sclerodactyly; Vascular - Raynaud phenomenon; Vascular - nailfold capillary abnormalities or digital-tip ulcers; Gastrointestinal - dysphagia or gastro-oesophageal reflux; Renal - renal crisis or new-onset arterial hypertension; and others.
The total is interpreted as: any score - Criteria not met: the major criterion (proximal skin sclerosis) is mandatory - without it juvenile systemic sclerosis cannot be classified; 4 criteria or more - Major only: major criterion present but fewer than 2 minor criteria - at least 2 minor criteria are required; 6 criteria or more - Criteria MET: major criterion plus ≥2 minor criteria - classifies as juvenile systemic sclerosis (sensitivity 90%, specificity 96%). Screen for pulmonary, cardiac and renal involvement at baseline.
No. It is a structured way to record and communicate severity. A clinician concerned about a child should act on that concern regardless of the total.
Onset must be before the 16th birthday for the juvenile classification.
Yes. Score definitions are bundled with the PediAid app, so the score computes without a connection.