Weighted classification criteria; a total of ≥ 4 classifies primary Sjögren syndrome.
The Sjögren Syndrome — ACR/EULAR 2016 is a rheumatology scoring tool used in paediatric practice. Weighted classification criteria; a total of ≥ 4 classifies primary Sjögren syndrome. It scores 5 criteria and interprets the total across 2 bands, so the number always arrives with the severity it implies rather than on its own. In PediAid each criterion is shown as a labelled option with the weight it carries, so the total can be checked rather than taken on trust.
5. They are Labial salivary gland biopsy with focal lymphocytic sialadenitis, focus score ≥ 1 foci/4 mm²; Anti-SSA/Ro antibody positive; Ocular staining score ≥ 5 (or van Bijsterveld ≥ 4) in at least one eye; Schirmer test ≤ 5 mm/5 min in at least one eye; Unstimulated whole saliva flow rate ≤ 0.1 mL/min.
The total is interpreted as: any score - Does not classify: total <4 - does not classify as primary Sjögren syndrome; 4 points or more - Classifies as Sjögren: total ≥4 - classifies as primary Sjögren syndrome (sensitivity 96%, specificity 95%). In children, recurrent parotitis is a more common presentation than sicca symptoms.
No. It is a structured way to record and communicate severity. A clinician concerned about a child should act on that concern regardless of the total.
Applies to patients with at least one symptom of ocular or oral dryness, or suspicion from the ESSDAI. Exclusions include prior head/neck radiation, active hepatitis C, AIDS, sarcoidosis, amyloidosis, GVHD and IgG4-related disease.
Yes. Score definitions are bundled with the PediAid app, so the score computes without a connection.